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https://www.selleckchem.com/pr....oducts/sch-527123.ht
The mPAP improved with either oral (57±17 pre-treatment versus 44±13mmHg post-treatment, p=0.03) or intravenous (80±15 pre-treatment versus 64±16mmHg post-treatment, p=0.017) therapy. PVR also improved with either oral (10±4 pre-treatment versus 6±3 WU post-treatment, p=0.004) or intravenous (17±5 pre-treatment versus 10±4 WU post-treatment, p=0.04) therapy. Survival among HHT-PAH patients who received oral or intravenous therapy was not different (p=0.2). Unadjusted survival among HHT-PAH patients was longer than that of IPAH patien

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